Hearing loss and retinitis pigmentosa are rarely found in combination. Therefore, most people who have retinitis pigmentosa and hearing loss probably have US1 or US2. Special tests such as electronystagmography (ENG) to detect balance problems and electroretinography (ERG) to detect retinitis pigmentosa help doctors to detect US early. Early diagnosis is important in order to begin special educational training programs to help the individual deal with the combined hearing and vision difficulties.
Original address of this page:
http://www.nih.gov/nidcd/health/pubs_hb/usher.htm#diagnosed