Usher Syndrome is an inherited disorder that is transmitted genetically by a recessive gene that is not sex linked. Both parents must carry the recessive gene for Usher Syndrome to produce a child with the disorder. More than 1/2 of the 16,000 deaf-blind people in the U.S. are believed to have Usher Syndrome.
3 per 100,000 people in the United States have Usher Syndrome. 3-6% of those with a congenital hearing loss have Usher Syndrome. In the 70,000-100,000 population with Retinitis Pigmentosa, 1 out of 4 people have Usher. USH1 and USH2 are the most common types of Usher Syndrome. USH1 and USH2 account for approximately 10% of all cases of children who are born deaf.
Original address of this page:
falcon.jmu.edu/~hayeske/usher.htm
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